产品货号：
Z28209
中文名称：
TIMM8A抗体
英文名称：
Anti-TIMM8A Antibody
产品规格：
50μl|100μl|150μl
发货周期：
1～3天
产品价格：
询价
| 抗体名称 | Anti-TIMM8A Antibody |
| 指标别名 | DDP;DDP1;Deafness dystonia protein 1;DFN1;MTS;TIM8;TIM8A;TIMM8A |
| 克隆性 | Polyclonal |
| 检验物种 | human,monkey,mouse,rat |
| 应用范围 | WB,IHC,ICC/IF,ELISA |
| 基因名称 | TIMM8A |
| 抗体来源 | Rabbit |
| 抗体类型 | IgG |
| 免疫原 | E.coli-derived human TIMM8A/DDP recombinant protein (Position:A14-D97). |
| 实际分子量 | 13～14KD |
| 成分 | 500μg/mL antibody with PBS，0.02% NaN3,1mg BSA and 50% glycerol. |
| 纯化方式 | Immunogen affinity purified. |
| 浓度 | 500μg/mL |
| 产品形态 | 溶液 |
| 保存条件 | 12 months from date of receipt，-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing. |
| 背景资料 | Mitochondrial import inner membrane translocase subunit Tim8 A,also known as Deafness-dystonia peptide or protein is an enzyme that in humans is encoded by the TIMM8A gene.This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane.The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system.Defects in this gene also cause Jensen syndrome;an X-linked disease with opticoacoustic nerve atrophy and muscle weakness.This protein,along with TIMM13,forms a 70kDa heterohexamer.Alternative splicing results in multiple transcript variants encoding distinct isoforms. |
| Uniprot ID | O60220 |
| 推荐配套试剂 | Biorab recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ZN1926) for Western blot. |
| 基因名全称 | translocase of inner mitochondrial membrane 8A |
| 蛋白名全称 | Mitochondrial import inner membrane translocase subunit Tim8 A |
| 推荐稀释比 | Western blot(WB) 1:500～2000 Immunohistochemistry in paraffin section (IHC) 1:50～400 Immunocytochemistry/Immunofluorescence (ICC/IF) 1:50～400 ELISA 1:100～1000 (Boiling the paraffin sections in 10mM citrate buffer,pH6.0,or PH8.0 EDTA repair liquid for 20 mins is required for the staining of formalin/paraffin sections.) Optimal working dilutions must be determined by end user. |
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